Pharmacological Improvement of Cystic Fibrosis Transmembrane Conductance Regulator Function Rescues Airway Epithelial Homeostasis and Host Defense in Children with Cystic Fibrosis.
American Journal of Respiratory and Critical Care Medicine(2024)
关键词
CF,CFTR modulation,single-cell RNA sequencing,airway inflammation,epithelial homeostasis
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